Marshall Smith Syndrome

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HollywdAnesth

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Has anyone here ever anesthetized a patient with Marshall Smith syndrome?

I had one dropped on me today. 20 male for ESWL at an outpatient surgery center.

I had never heard of it before and luckily Google books brought this up

http://books.google.com/books?id=2Z...A#v=onepage&q=marshall smith syndrome&f=false

The child had severe craniofacial abnormalities, and has had a trach since we was an infant. According to his parents, his cardiac studies have all been normal. As have his cervical spine studies done by his neurosurgeon. He does have severe scoliosis.

I sucked out his G tube. "Mask" induced over his uncuffed shiley trach. Once he was asleep, I removed the shiley and placed a cut 6.0 ETT into his stoma, and inflated the cuff. He desatted in a hurry to the 70s during this. Kept him breathing spotaneously. No narcotics, just a bit of zofran. 30 min of ESWL, woke him up and replaced the ETT with his original shiley.

He spent 15 min in the PACU and went home.

Anybody have any experience with these patients?
Did I do a crappy job?

This site was also helpful.
http://www.marshallsmith.org/en/what-is-mss
 
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